Review Article

IgG4 Related Sclerosing Cholangitis

Table 2

Classification of IgG4 related sclerosing cholangitis (IgG4-SC), differential diagnosis, and investigations (modified from the study by Nakazawa et al. [32]).

ā€‰CholangiogramDifferential diagnosisInvestigations

Type 1PCa
CCa
CP
EUS-FNA
Endobiliary brushings
Endobiliary biopsies
Percutaneous biopsy

Type 2PSCLiver biopsy
Colonoscopy (i.e. look for concurrent IBD)

Type 3CCa
GB cancer
EUS
Endobiliary biopsy
Percutaneous biopsy
Type 4